Pulmonary veno-occlusive disease is an extremely rare form of high blood pressure in the lung area.
See also: Primary pulmonary hypertension
In most cases, the cause of pulmonary veno-occlusive disease is unknown. The condition may be related to a viral infection. It may occur as a complication of certain diseases such as lupus, or as a complication of leukemia, lymphoma, chemotherapy, or bone marrow transplantation.
The disorder is most common among children and young adults. As the disease gets worse, it causes narrowed pulmonary veins, pulmonary artery hypertension, and congestion and swelling of the lungs.
The doctor will perform a physical exam.
The exam may reveal:
Your doctor may hear abnormal heart sounds when listening to the chest and lungs with a stethoscope.
The following tests may be done:
There is currently no known effective medical treatment. However, the following medications may be helpful for some patients:
A lung transplant may be needed.
The outcome is often very poor in infants with a survival rate of just a few weeks. Survival may be months to a few years in adults.
Call your health care provider if you have symptoms of this disorder.
Pulmonary vaso-occlusive disease